5 Facts you should know about

Keratoglobus

Clinical presentation is characterized by progressive diminution resulting from irregular corneal topography with increased corneal fragility due to extreme thinning

Corneal pathology causes severe visual impairment including extreme myopia, irregular astigmatism, and corneal scarring

If afflicting both eyes, the deterioration in vision can affect the patient's ability to drive a car or read normal print. It does not however lead to blindness

it is typically diagnosed in the patient's adolescent years and attains its most severe state in the twenties and thirties

The congenital form is more common - it is associated with Ehler-Danlos type VI, Leber congenital amaurosis, and the blue sclera syndrome

See our full disease profile

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